Solitary fibrous tumor (SFT) is a rare mesenchymal tumor with an intermediate tendency to metastasize, which is found in many different locations including head and neck, abdomen, chest cavity and extremities. Also, meningeal hemangiopericytoma (HPC) is considered an SFT which arises in the meningeal membranes. SFT family shows an undetermined biologic behavior varying from a silent indolent tumor to an aggressive malignant form; however, benign and malignant variants of SFT may have similar cytopathologic characteristics. In this study, we defined the factors correlated with SFT's aggressive behavior and patient's survival.

This is a retrospective study based on medical records of 85 patients who were suffering from SFT and had been treated at McGill University Health Centre (MUHC) between 1984 and 2017. We used multivariate logistic regression analysis to address any association between the variables including patient's demographics, tumor size, primary location of the tumor, pathological features, treatment methods and outcomes.

The median of the follow-up period was 60 months. The patient's age or gender had no association with tumor aggressive behavior or patient's survival. Anatomical origin of primary tumor had no strong correlation with the patient's disease related death (DRD); however, tumors originated from CNS showed more aggressive behavior. There was an association between tumor size more than 7 cm and distant metastasis (MT) (p= 0.03) and DRD (p=0.03). The tumor size also correlated with the 5-year disease-free survival (p=0.017). We had three histologic groups: 1- Benign SFT (30 cases), 2- cellular SFT or HPC (29 cases), 3- malignant SFT or anaplastic HPC (26 cases). Although univariate analysis demonstrates that patients suffering from cellular SFT and malignant SFT showed increased aggressive behavior of the tumor, multivariate analysis didn't verify the mentioned association. Patients with positive margins had increased odds ratio to experience tumor local recurrence (LR) (p= 0.05) and LR was correlated with DRD in our patients (p=0.006). Radiotherapy had no statistical association with LR, MT or DRD. Frequency of LR and MT in the study were 25.7% and 29.8% respectively. 5-year disease-free survival in our patients was 76%.

The size of SFT is the most correlative predictor of the tumor's aggressive behavior. The local recurrence of SFT is associated with disease related death; therefore, resection of the tumor with negative margins provides the highest chance of cure. In addition, a cellular SFT should be treated like a malignant variant of the tumor.

Introduction

The proximal femur fracture in children is rare. Furthermore osteoporotic fracture associated with bone tumor make it difficult to decide the proper management method. The treatment plan should include both the treatment of the fracture and management of the condition responsible for the fracture. However, the reported literatures are rare and vary.

In distal fibular resection without reconstruction, the stabilising effect of the lateral malleolus is lost. Thus, the ankle may collapse into valgus and may be unstable in varus. Here, we describe a child who underwent successful staged surgical correction of a severe neglected valgus deformity after excision of the distal fibula for a Ewing’s sarcoma.

The purpose of this study was to determine the annual incidence of Perthes’ disease in Korea and compare this with other populations. A survey identified all newly diagnosed children with Perthes’ disease aged 14 years or younger in South Honam, Korea, between January 1999 and December 2001. A total of 84 children were included: 29 in 1999, 28 in 2000 and 27 in 2001. The mean annual incidence was 3.8 per 100 000. This is similar to that reported in other Asian countries, but higher than in black populations and lower than in Caucasians.

Introduction: The incidence of Legg-Calvé-Perthes Disease (LCPD) has varied considerably both between countries and between population groups. The incidence of LCPD has not been reported in Korea. The purpose of this study was to determine the annual incidence of LCPD in Korea and to compare this to other population groups.

Materials and Methods: Firstly, only LCPD children who were living in Chonnam Province, Korea, and were aged 14 years and under during the years 1999, 2000, and 2001, were reviewed to measure the annual incidence. Secondly, for a further study regarding the variables related to the epidemiological interest, 816 hips, which were treated at our hospital during the last 32 years from 1972 to 2003, were reviewed.

Results: The population aged 14 years and under was 734,645 in 1999, 728,721 in 2000, and 719,504 in 2001. Among them, the number of LCPD children was 29 in 1999, 28 in 2000, and 24 in 2001. The annual incidence was 3.9 per 100, 000 in 1999, 3.8 in 2000, and 3.3 in 2001, with a mean incidence of 3.7 per 100, 000.

Discussion: The annual incidence of LCPD in Korean children aged 14 years and under was 3.7 per 100,000. This Korean incidence was lower than the 5.1 to 21.1 per 100,000 incidence reported in Caucasians and higher than the 0.45/100,000 reported in blacks or mixed decent. The incidence of gender, bilaterally, age of disease onset, extent of head involvement, and other related epidemiological parameters was similar to those reported in other studies.

Introduction: Shortening of the affected limb has frequently been observed in children with Legg-Calvé-Perthes disease (LCPD). Many factors have been thought as the cause of this residual shortening after LCPD. There has been no clear answer regarding which is more responsible for the residual shortening between coxa plana and the disturbed physeal growth. To clarify the main cause of residual shortening, clinical and experimental studies were conducted.

Materials and Methods: For clinical study, 40 LCPD children with definite shortening were evaluated. This included 20 children with active disease and 20 children at skeletal maturity. Teleoroentgenograms were obtained for all children. For the experimental study, LCPD simulation in 30 piglets was achieved by disrupting the blood supply to the capital femoral epiphysis.

Results: In the clinical study, total shortening in the skeletal maturity group was 14.6 mm, which consisted of 3.2 mm (16%) shortening by decreased epiphyseal height and 11.5 mm (84%) shortening by physeal growth disturbance. Total shortening in the active disease group was 7.9 mm, which consisted of 6.4 mm (84%) decrease of epiphyseal height and 1.5 mm (16%) shortening by physeal growth disturbance. In the experimental study, overall shortening (13.6 mm) in the piglet model showed a predominance of disturbed physeal growth. The proportions were 3.2 mm (24%) by epiphyseal height decrease and 10.4 mm (76%) by physeal growth disturbance.

Conclusion: Physeal growth disturbance was mostly responsible for the residual shortening following LCPD. However, in the stages of active disease, the shortening of the extremity was mainly caused by a decrease of epiphyseal height.

Purpose: The prospective study conducted by an independent examiner included an overall series of 104 ligamento-plasties using the fascia lata (Jaeger procedure).

Material and methods: All procedures were performed by the same operator and outcome was assessed at least 12 months after operation (mean follow-up 27 months).

Results and discussion: The IKDC scores were comparable with other series using autotransplants: 39% A, 45% B, 12% C, 4% D. Mean residual laxity differential (KT 2000) was 1.92 mm (−2 to 6 mm) and showed the anatomic efficacy of this technique. Extra-articular reinforcement was determinant in supporting the intra-articular plasty, calibrated at 6 mm diameter, explaining the good score obtained for residual differential laxity in sub-extension: 54% A, 29%B, 3%C. Laxity measured between +2 and +3 mm in 14% of the patients who could not be classed in the IKDC A and B classes. Mixed plasty with the fascia lata neutralised rotation clicks in 90.4% of the cases. The lateral portion of the mixed plasty did not raise any problem for ligamentisation explaining its efficacy and low rate of rotation clicks at last follow-up.

All professional athletes in this series and all athletes participating in high-level competitions were able to resume their former sports activity at the same level; for the entire series 67% resumed their former sports activities at the same level. Thirty-eight competition level athletes (n=63, 60%) resumed competition after surgery, 24 (38%) practised leisure sports. The change to leisure sports in these 24 patients was related to the knee plasty in eight. Irreducible knee flexion (+5°) was related to reflex dystrophy in four patients. Eleven patients presented reflex dystrophy; two had mobilisation under general anaesthesia.

None of the patients had a painful harvesting site. Among the four cases with lateral decoaptation, two were related to poor dissection of the posterolateral angle without any pre-existing lesion of the peripheral formations.

Section of the lateral intermuscular partition allowed complete closure of the fascia lata in all the difficult cases. We had only one case of proximal muscular herniation at the harvesting site.