Aims: Extraskeletal bone tumours are rare and high-grade tumours including osteosarcoma (OS), chondrosarcoma (CHO) and Ewingñs sarcoma (EW) of the soft tissues and its variants. A retrospective study of 22 cases were made in our Hospital in the period from 1983–2000. Methods: The study of 22 cases revealed that this tumours affect adults (median age 50.86; range 17 to 70 years). The thigh (36.36%) and the arm-elbow (18.18%) were the most common tumour locations. For diagnostic type of tumours 11 were CHO, 8 OS and 3 EW. The median follow-up was 48.9 months with a range 6 to a97 months. All of the cases of OS and EW were treated with preoperative chemotherapy and postoperative radiotherapy. Results: The preoperative duration of symptoms was ranged from 6 weeks to 6 years (median 6 months). Local recurrences after wide and radical surgery developed in 8 cases Ð35.45%- (3 CHO, 4 OS and 1 EW) and distant metastases developed in 3 cases (13.18%). 14 cases were alive with no evidence of recurrence (63.6%), 5 were alive with one or more recurrences (22.72%), 1 were alive with metastases (4.59%) and 2 ulcerated tumours were exitus form metastases (10.05%). Five amputations were performed. Conclusions: 1. All cases were high-grade tumours. 2. The prevailing sites of metastases were the lung, the regional lymph nodes and the skeleton. 3. Cure may be achieved by wide or radical local excision of the tumour at and early stage of the disease (combined with radiation and chemotherapy).