Abstract
Purpose of Study
To see if the addition of a locking plate to FD rod fixation of osteogenesis imperfecta confers extra strength and allows earlier mobilisation.
Introduction
Osteogenesis imperfecta is a heterogeneous group of disorders with congenital osseous fragility. The goal of surgery is to minimise the incidence of fracture and correct deformity. The concept of multilevel osteotomies and intramedullary fixation with a non-extendable nail was popularised by Sofield and Millar in 1959. The Bailey Dubow telescoping nail was introduced in 1963. The Fassier-Duval (FD) telescoping nail is a more recent design inserted via smaller incisions, in conjunction with percutaneous osteotomies. However there are still problems. Often the medullary canal may be too narrow to harbour a nail of adequate size for the body. Furthermore they do not give significant rotational control, which is compounded by the elasticity of the soft tissues.
Methods
We treated two patients with Osteogenesis imperfecta with supplementary unicortical locked plating in addition to intramedullary fixation with FD rods.
Results
The patients both underwent femoral fixation. Both had deformity and previous femoral stress fractures treated non operatively. One patient, aged 24, was non ambulant pre-operatively. She was allowed to transfer without a brace immediately post operatively. The other patient, aged 64 years and ambulant indoors, initially had additional fixation with a non- locking semitubular plate that went onto fail, therefore had revision fixation with a locking plate. She was asked to bear weight as tolerated in a brace immediately post-op.
Conclusion
Classically, plates and screws have been avoided in Osteogenesis imperfecta due to the predisposition to fracture at the ends of the plate. We have found that the extra fixation enables extra strength where the nail size is small, and helps control rotation in the post-operative period, allowing earlier mobility.
