Abstract
Study Design: Case Report
Purpose: To evaluate the role of using VEPTR™ to treat kyphosis in children with Hurler’s syndrome.
Summary of Background Data: Spinal manifestations are common in children with mucopolysaccridosis (MPS) and likely to increase with advances in bone marrow transplantation. However, no optimal treatment exists in treating kyphosis in children with MPS. VEPTR™ has not been previously used in children with MPS.
Methods: Evaluate the early results of one ambulating child with Hurlers syndrome who underwent treatment for their kyphosis using VEPTR™
Results: Early results at 7 months are excellent, despite an initial wound infection treated with dressing and antibiotics. No concerns arise with their gait and they have undergone their first lengthening. Excellent correction of their kyphosis has been achieved.
Conclusion: VEPTR™ offers an excellent implant in treating a selective group of children with MPS, who may have previously been declined surgery. To our knowledge this is the first case where this technique has been attempted on an ambulating MPS child.
Ethics Approval: None
Interest Statement: None
Correspondence should be addressed to BSS c/o BOA, at the Royal College of Surgeons, 35–43 Lincoln’s Inn Fields, London, WC2A 3PE, England.
