Abstract
Purpose: Congenital proximal radioulnar synostosis is a rare anomaly of failure of segmentation of the radius and ulna resulting in a fixed rotational position of the forearm from neutral to maximum pronation. Several surgical options have been proposed for the treatment of this condition. We have treated six forearms in five children with pronation deformity using derotational osteotomies of the radius and ulna with postoperative wire stabilisation of the ulna. The surgical technique and results of treatment with this method are presented.
Methods: With this technique, osteotomies were performed at the midshaft of the ulna and the distal diaph-yseal-metaphyseal junction of the radius. The insertion of intramedullary Ilizarov wires facilitated manual derotation of the radius and ulna to a functional position of 100 supination of the forearm. Postoperatively, the forearm was immobilised in a cast for an average of 6.3 weeks and the wire was removed when there was evidence of union. 3 boys and 2 girls with a mean age of 4.9 years underwent surgery with this method and were followed-up for an average of 29 months (range 12 to 43 months).
Results: Forearm position improved from an average pronation deformity of 68.3 degrees to the pre-planned position of 100 degrees supination in all cases. Bone union was achieved in all six forearms by 6.3 weeks. At their most recent follow-up, there was no loss of correction evident in any of the patients. There was one complication, namely haematoma formation at the radial osteotomy site mimicking compartment syndrome and requiring exploration, although no soft tissue compromise was evident.
Conclusion: The principal advantages of this technique include the ease of the surgical approach for the distal radial osteotomy, the longterm maintenance of rotational correction and the need for single wire stabilisation of the ulna only, which in theory reduces the potential risk of implant-related complications. We conclude that this modified forearm derotational osteotomy with wire stabilisation of the ulna alone is a safe and effective method for treating pronation deformity in children with congenital proximal radioulnar synostosis, although vigilance for early soft tissue complications is necessary.
Theses abstracts were prepared by Professor Roger Lemaire. Correspondence should be addressed to EFORT Central Office, Freihofstrasse 22, CH-8700 Küsnacht, Switzerland.
