Abstract
To report on previously unreported behaviour of a rare condition and to recommend suitable management.
Fibrous periosteal tethers are a rare but recognised cause of angular growth deformity, usually of the femur. The periosteum is thought to act as a brake to growth, and unilateral tethering has been shown to cause angular growth deformity experimentally, although the aetiology of periosteal tethers is obscure.
Nine cases have previously been reported, all of which were progressive and none of which were present at birth. All required release of the tether and all but one required osteotomy to correct deformity. It has been thought that periosteal tethering might remodel if allowed to and that, if periosteal release were carried out, the deformity might correct without the need for osteotomy. However, this has never been reported.
We report two cases of periosteal tethering, well demonstrated on MRI which were remarkable in that they were present at birth. Neither child had any history of an intrauterine event or any other pathology. One involved the tibia, which remodelled without intervention. This is the first ever report of a tibial periosteal tether, and the tether could clearly be seen to be reabsorbed as the tibia remodelled. The other involved the ulna, which corrected after release of the tether alone.
Periosteal tethering can affect children of any age and has the potential to remodel without intervention. We therefore recommend a period of observation first if the deformity is not progressive. If the deformity is progressive, then early release of the tether is recommended. If this path is followed then it is likely that osteotomy would not be required. M.R.I. demonstrates the tether well and is the investigation of choice for this condition.
The abstracts were prepared by Mr Richard Buxton. Correspondence should be addressed to him at Bankton Cottage, 21 Bankton Park, Kingskettle, Cupar, Fife KY15 7PY, United Kingdom
